Аннотация:
Neural tube defects are the most common central nervous system malformation. Dandy-Walker malformation (DWM) is a rare abnormality of the posterior cranial fossa, which is generally diagnosed in the prenatal period or early infancy. The paper describes a case of the late clinical manifestation of DWM, which has caused syringomyelia. All variants of pathological changes within the Dandy-Walker complex very rarely become a cause of syringomyelia. Only four cases of DWM, in which syringomyelia was found in adults, are known. The authors believe that formation of syringomyelia cysts in these patients is associated with the impaired circulation of normal cerebrospinal fluid between the superior cistern and the subarachnoid spaces of the spinal cord due to the caudal dislocation of the cyst formed in the fourth ventricle. Decompression of the craniovertebral junction, by resecting the caudal portion of the cyst in the foramen magnum, and repair of the free communication between the superior
Евзиков Г. Ю. Григорий Юльевич 1962-
Башлачев М. Г. Михаил Григорьевич 1991-
Белозерских К. А. Константин Александрович 1991-
Парфенов В. А. Владимир Анатольевич 1957-
Evzikov G. Yu. Grigorij Yulyevich 1962-
Bashlachev M. G. Mikhail Grigoryevich 1991-
Belozerskikh K. A. Konstantin Aleksandrovich 1991-
Parfenov V. A. Vladimir Anatolyevich 1957-
Dandy-Walker malformation is a rare cause of syringomyelia in adults
Текст визуальный непосредственный
Неврология, нейропсихиатрия, психосоматика
ИМА-Пресс
Т. 9, Вып. 3 С. 62-67
2017
Статья
Dandy-Walker malformation Late clinical manifestation Syringomyelia
Neural tube defects are the most common central nervous system malformation. Dandy-Walker malformation (DWM) is a rare abnormality of the posterior cranial fossa, which is generally diagnosed in the prenatal period or early infancy. The paper describes a case of the late clinical manifestation of DWM, which has caused syringomyelia. All variants of pathological changes within the Dandy-Walker complex very rarely become a cause of syringomyelia. Only four cases of DWM, in which syringomyelia was found in adults, are known. The authors believe that formation of syringomyelia cysts in these patients is associated with the impaired circulation of normal cerebrospinal fluid between the superior cistern and the subarachnoid spaces of the spinal cord due to the caudal dislocation of the cyst formed in the fourth ventricle. Decompression of the craniovertebral junction, by resecting the caudal portion of the cyst in the foramen magnum, and repair of the free communication between the superior